Change in nutrient and dietary intake in european children with cystic fibrosis after a 6-month intervention with a self-management mhealth tool

Joaquim Calvo-Lerma*, Mieke Boon, Jessie Hulst, Carla Colombo, Inês Asseiceira, María Garriga, Etna Masip, Ine Claes, Anna Bulfamante, Hettie M. Janssens, Maria Roca, Saioa Vicente, Victoria Fornés, Laura Zazzeron, Bo van Schijndel, Sandra Woodcock, Luisa Pereira, Kris de Boeck, Carmen Ribes-Koninckx

*Corresponding author for this work

Research output: Contribution to journalArticleAcademicpeer-review

8 Citations (Scopus)
77 Downloads (Pure)


Cystic Fibrosis (CF) is a life-long genetic disease, causing increased energy needs and a healthy diet with a specific nutrient distribution. Nutritional status is an indicator of disease prognosis and survival. This study aimed at assessing the effectiveness of a self-management mobile app in supporting patients with CF to achieve the dietary goals set by the CF nutrition guidelines. A clinical trial was conducted in pancreatic insufficient children with CF, followed in six European CF centres, where the self-management app developed within the MyCyFAPP project was used for six months. To assess secondary outcomes, three-day food records were compiled in the app at baseline and after 3 and 6 months of use. Eighty-four subjects (mean 7.8 years old) were enrolled. Compared to baseline, macronutrient distribution better approximated the guidelines, with protein and lipid increasing by 1.0 and 2.1% of the total energy intake, respectively, by the end of the study. Consequently, carbohydrate intake of the total energy intake decreased significantly (−2.9%), along with simple carbohydrate intake (−2.4%). Regarding food groups, a decrease in ultra-processed foods was documented, with a concomitant increase in meat and dairy. The use of a self-management mobile app to self-monitor dietary intake could become a useful tool to achieve adherence to guideline recommendations, if validated during a longer period of time or against a control group.

Original languageEnglish
Article number1801
Issue number6
Publication statusPublished - 26 May 2021

Bibliographical note

Funding Information:
Acknowledgments: The authors acknowledge the European Union’s funding to conduct this project and especially thank the participants and their families for their effort and enthusiasm.

Funding Information:
Funding: This research was funded by the Horizon 2020 Research and Innovation Framework Programme of the European Union (PHC-26-2014, Self-management of health and disease: citizen engagement and mHealth), grant number 643806.

Publisher Copyright:
© 2021 by the authors. Licensee MDPI, Basel, Switzerland.

Research programs

  • EMC OR-01-54-02


Dive into the research topics of 'Change in nutrient and dietary intake in european children with cystic fibrosis after a 6-month intervention with a self-management mhealth tool'. Together they form a unique fingerprint.

Cite this