TY - JOUR
T1 - Long-term follow-up after repair of Ebstein's anomaly
AU - Palmen, M (Meindert)
AU - de Jong, P.L.
AU - Klieverik, Loes
AU - Venema, Angeliek
AU - Meijboom, FJ (Folkert)
AU - Bogers, Ad
PY - 2008
Y1 - 2008
N2 - Objective: We studied the long-term results of vertical plication repair of Ebstein's anomaly according to Carpentier. Methods: Between 1988 and 2007, 28 patients (mean age 28.8 +/- 15.7 years, range 4-58 years) underwent vertical plication repair of Ebstein's anomaly. At operation the anomaly was classified according to Carpentier. In three patients (11%) a cavopulmonary shunt was added at the repair on the indication of impaired right ventricular function. Results: There was no operative mortality. Early mortality was 3.6% (one patient). Actuarial survival and actuarial freedom from reoperation at 19 years were 96% (95% Cl; 96-97%) and 72% (95% Q 53-92%), respectively. Six patients required reoperation, with a successful re-repair in three patients. Mean duration of follow-up was 10.7 +/- 6.5 years. One year postoperatively, tricuspid incompetence had decreased significantly (p < 0.001), as had New York Heart Association (NYHA) functional class (p < 0.001). In addition, exercise tolerance had increased (70 +/- 19% to 92 +/- 9% of predicted values, p < 0.05). Both tricuspid function and NYHA functional class remained essentially unchanged at the end of follow-up, indicating durable haemodynamic and functional results. Conclusion: This study demonstrates favourable tong-term results following vertical plication repair of Ebstein's anomaly with tow mortality, acceptable morbidity and good haemodynamic and functional results. (C) 2008 European Association for Cardio-Thoracic Surgery. Published by Elsevier B.V. All rights reserved.
AB - Objective: We studied the long-term results of vertical plication repair of Ebstein's anomaly according to Carpentier. Methods: Between 1988 and 2007, 28 patients (mean age 28.8 +/- 15.7 years, range 4-58 years) underwent vertical plication repair of Ebstein's anomaly. At operation the anomaly was classified according to Carpentier. In three patients (11%) a cavopulmonary shunt was added at the repair on the indication of impaired right ventricular function. Results: There was no operative mortality. Early mortality was 3.6% (one patient). Actuarial survival and actuarial freedom from reoperation at 19 years were 96% (95% Cl; 96-97%) and 72% (95% Q 53-92%), respectively. Six patients required reoperation, with a successful re-repair in three patients. Mean duration of follow-up was 10.7 +/- 6.5 years. One year postoperatively, tricuspid incompetence had decreased significantly (p < 0.001), as had New York Heart Association (NYHA) functional class (p < 0.001). In addition, exercise tolerance had increased (70 +/- 19% to 92 +/- 9% of predicted values, p < 0.05). Both tricuspid function and NYHA functional class remained essentially unchanged at the end of follow-up, indicating durable haemodynamic and functional results. Conclusion: This study demonstrates favourable tong-term results following vertical plication repair of Ebstein's anomaly with tow mortality, acceptable morbidity and good haemodynamic and functional results. (C) 2008 European Association for Cardio-Thoracic Surgery. Published by Elsevier B.V. All rights reserved.
U2 - 10.1016/j.ejcts.2008.03.048
DO - 10.1016/j.ejcts.2008.03.048
M3 - Article
C2 - 18455420
SN - 1010-7940
VL - 34
SP - 48
EP - 54
JO - European Journal of Cardio-thoracic Surgery
JF - European Journal of Cardio-thoracic Surgery
IS - 1
ER -