Nuclear DNA origin of mitochondrial complex I deficiency in fatal infantile lactic acidosis evidenced by transnuclear complementation of cultured fibroblasts

V Procaccio, B Mousson, R Beugnot, H Duborjal, F Feillet, G Putet, I Pignot-Paintrand, A Lombès, IFM Coo, HJM Smeets, J Lunardi, J-P Issartel

Research output: Contribution to journalArticleAcademicpeer-review

32 Citations (Scopus)
Original languageUndefined/Unknown
Pages (from-to)83-92
Number of pages10
JournalJournal of Clinical Investigation
Volume104
Issue number1
Publication statusPublished - 1999

Research programs

  • EMC MM-04-44-02

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